Author: Jeeya Shah and Nirmal Sharma
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Thalassemia major is a blood disorder of inheritance that is transmitted from parents to offspring, resulting in incapacity to produce an adequate quantity of haemoglobin and severe haemolytic anaemia. These conditions are extremely prevalent single-gene disorders in India. Patients with thalassemia require lifelong regular blood transfusion, typically beginning prior to being 2 years old, and die within ten-twenty years if untreated. The purpose of this investigation is to determine the prevalence and availability of blood transfusions among thalassemia patients in India. The challenge is that the illness is severely impacted by the adverse effects of transfusions, which must be assessed and managed throughout life. Blood transfusion exposes patients to adverse events like nonhemolytic cold, along with allergic, and also delayed reactions to a blood transfusion, transfusion-related lung injury, along with graft-versus-host illness, and the transfusion of pathogenic organisms including viruses, bacteria, and parasites. The prevalence of thalassemia differs as the geographical location changes and availability of blood transfusions depending on different awareness program, which is a part of management of blood transfusion for Thalassemia patients.
Blood transfusion, Thalassemia, India, Patients, Availability, Practices
Although substantial data on the incidence of thalassemia carriers is accessible from a few states in India, much of it is hospital-based along with selective, making it difficult to estimate the true disease burden. In India, transfusion care for Hb disorder patients should continue to emphasize education and awareness. During viral pandemics, it is essential that blood depots and transfusion facilities remain operational for the sake of other patients. During these pandemics, blood banks along with transfusion centres must devise strategies to preserve blood supply. A team-based strategy is essential for conquering the present obstacles. With the imminent implementation of a national thalassemia control program and the availability of blood transfusions, adequate centres for assessment and suitable quality control would be recognized, and a multitude of trained ancillary workers and genetic counsellors will be needed.
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